Synonyms: 3-Methyl-2-pentenedioic acid; NSC 249232
Molecular Formula: C6H8O4
Molecular Weight: 144.13
Linear Structural Formula: C6H8O4
MDL Number: MFCD01556044
Purity: >=98.0% (HPLC)
Storage: 2-8C
Biochem Physiol Actions: 3-Methylglutaconic acid is a metabolite (as the CoA thioester) in the leucine degradative pathway as well as the mevalonate shunt, a pathway that links isoprenoid metabolism with mitochondrial acetyl-CoA metabolism. 3-Methylglutaconic acid accumulates in patients with a deficiency of 3-methylglutaconyl-CoA hydratase.